REDUCED GLOBAL LONGITUDINAL STRAIN IS AN EARLY DIAGNSTICAL SIGN OF VENTRICULAR DYSFUNCTION IN COMPLEX CONGENITAL HEART DEVICE (BERRY SYNDROME). DESCRIPTION OF A CLINICAL CASE

Sakovich Vitaliy Valerievich, Drobot Dmitry Borisovich, Gankin Mark Isakovich

According to 2-D echocardiography, the child with Berry syndrome had no signs of dilation or hypoplasia of the heart chambers, no signs of their dysfunction (LVEF 67%, RV FI 35%). However, a decrease in the longitudinal deformation of the ventricular myocardium was detected (GLS LV -15, GLS RV -18). The child underwent urgent radical surgery: Formation of an anastomosis between the ascending and descending aorta. Closure of the aortopulmonary window with an Ecoflon patch. Ligation of the patent ductus arteriosus. Suturing of the atrial septal defect. The postoperative period was uneventful. The child was transferred from the intensive care unit on the 2nd day, discharged from the hospital on the 9th day after the surgery in a satisfactory condition, without signs of heart failure. 2D echocardiography parameters and ventricular longitudinal deformation parameters corresponded to the normative ones (LVEF 66%, RV EF 44%, LV GLS -21, RV GLS -22).

Keywords:aortopulmonary window, aortopulmonary septal defect, aortic arch rupture, open ductus arteriosus with retrograde blood discharge, global longitudinal strain.